IMMUNOLOGY TEXTBOOK - Mercury Podillia 2013

INNATE IMMUNE DEFICIENCY

ICD-10 Classification of Hereditary Immunodeficiencies

D80 Immunodeficiencies with predominantly antibody defects:

D80.0 Hereditary hypogammaglobulinemia;

D80.1 Nonfamilial hypogammaglobulinemia;

D80.2 Selective deficiency of immunoglobulin A [IgA];

D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses;

D80.4 Selective deficiency of immunoglobulin M [IgM];

D80.5 Immunodeficiency with increased immunoglobulin M;

D80.6 Antibody deficiency with near-normal IMMUNOGLOBULINS or with hyperimmunoglobulinemia;

D80.7 Transient hypogammaglobulinemia of infancy;

D80.8 Other immunodeficiencies with predominantly antibody defects;

D80.9 Immunodeficiency with predominantly antibody defects, unspecified.

D81 Combined immunodeficiencies:

D81.0 Severe combined immunodeficiency with reticular dysgenesis;

D81.1 Severe combined immunodeficiency with low T- and B-Cell numbers;

D81.2 Severe combined immunodeficiency with low or normal B-cell numbers;

D81.3 Adenosine deaminase deficiency;

D81.4 Nezelof syndrome;

D81.5 Purine nucleoside phosphorylase deficiency;

D81.6 Major Histocompatibility Complex Class I deficiency;

D81.7 Major histocompatibility complex class II deficiency;

D81.8 Other combined immunodeficiencies;

D81.9 Combined immunodeficiency, unspecified;

D82 Immunodeficiency associated with other major defects:

D82.0 Wiskott-Aldrich syndrome;

D82.1 DiGeorge syndrome;

D82.2 Immunodeficiency with short-limb stature;

D82.3 Immunodeficiency following hereditary defective response to Epstein-Barr virus;

D82.4 Hyper-immunoglobulin E [IgE] syndrome;

D82.8 Immunodeficiency associated with other specified major defects;

D82.9 Immunodeficiency associated with major defect, unspecified;

D83 Common variable immunodeficiency:

D83.0 Common variable immunodeficiency with predominant abnormalities in B-cell number and function;

D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders;

D83.2 Common variable immunodeficiency with autoantibodies to B or T Cells;

D83.8 Other common variable immunodeficiencies;

D83.9 Common variable immunodeficiency, unspecified.

D84 Other immunodeficiencies:

D84.0 Lymphocyte function-associated antigen-1 [LFA-1] defect;

D84.1 Defects in The Complement System;

E70.3 Chediak-Higashi syndrome (Steinbrinck).

D71 Functional disorders of polymorphonuclear neutrophils.

G11.3 Ataxia-telangiectasia (Louis-Bar syndrome).